Ictiose arlequim – manejo do nascimento aos 3 anos de idade
DOI:
https://doi.org/10.11606/issn.1679-9836.v99i4p411-414Palavras-chave:
Ictiose lamelar, Anormalidades congênitas, Dermatologia, PediatriaResumo
A ictiose arlequim possui uma prevalência de 1/100.000 nascimentos e é frequente o óbito ocorrer no período neonatal. Objetivo: descrever um caso em que o tratamento adequado permitiu a sobrevida da paciente. Descrição do caso: Recém-nascido (RN) do sexo feminino com 2665g, nasceu com placas hiperceratósicas e fissuras difusas pelo corpo, ectrópio bilateral com oclusão palpebral, eclábio e pés e mãos fletidos características de Ictiose congênita do tipo arlequim. O acitretin foi iniciado aos 7 dias de vida associado ao tratamento suportivo, evitando o óbito neonatal. Comentários: Atribui-se a sobrevida da paciente à intervenção com acitretin oral precoce e os cuidados intensivos neonatais.
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Referências
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