Linear scleroderma en coup de sabre in a teenager - a case report
DOI:
https://doi.org/10.11606/issn.1679-9836.v101i6e-195098Keywords:
Localized scleroderma, Morphea, Diseases of the skin and connective tissue, Skin diseasesAbstract
Scleroderma is an autoimmune disease identified by a progressive tightening of the skin. Scleroderma linear “en coup de sabre” is an unusual and uncertain cause, which in this form can cause progressive focal craniofacial atrophy. This disease is a rare condition that affects mainly children, in some cases besides that cutaneous findings, can result in comorbidity associated with the central nervous system. We describe the case report of a teenage boy (15 years old) with a complaint of the appearance of a hypochromic lesion with progressive growth in the frontal region. The diagnosis was confirmed by capillaroscopy, a dermatological physical exam of the affected area, incisional skin biopsy, and laboratory tests. Oral prednisone in association with topical clobetasol was used as a choice treatment, obtaining satisfactory clinical results with good response and a significant reduction in hypochromia. At the present, this is a rare disease with a lack of knowledge and some health professionals do not understand its difficulties, this report aims to demonstrate the importance of an early diagnosis and adequate clinical treatment to reduce active inflammation of the disease and morbidities, which can significantly reflect on the quality and life span of patients with this rare disease.
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