Madelung's disease (multiple symmetric lipomatosis)
case report
DOI:
https://doi.org/10.11606/issn.2176-7262.v52i4p355-360Keywords:
Lipomatosis, Madelung's Disease, Multiple Symmetrical LipomatosisAbstract
Study: The present study is a case report, carried out based on a review of medical records, authorized by the ethics committee of the hospital, and the informed consent form signed by the patient.
Importance: Madelung disease or multiple symmetric lipomatosis is a rare disorder of undefined aetiology, often associated with alcoholism and characterized by the presence of non-encapsulated symmetrically distributed adipose tissue masses, mainly in the upper trunk and cervical regions, which progressively increase which progressively increase size and lead to cosmetic disfigurement of the patient. It can cause symptoms arising from compression of vascular, nervous and aerodigestive tract structures. Lipectomy and liposuction are the treatments of choice, although generally palliative.
Comments: The present paper reports a case of Madelung's disease and presents a brief review of the literature on the subject, emphasizing the importance of clinical recognition of this entity, as well as its multidisciplinary management.
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